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Report

Intravenous immunoglobulin treatment in a type 3 von Willebrand disease patient with alloantibodies and a life-threatening gastrointestinal bleed.

  • Authors : Nummi V; Faculty of Medicine, University of Helsinki, Helsinki, Finland.; Coagulation Disorder Unit, Department of Hematology and Comprehensive Cancer Center, Helsinki University Hospital, Helsinki, Finland.

Subjects: Gastrointestinal Hemorrhage/Gastrointestinal Hemorrhage/Gastrointestinal Hemorrhage/*complications ; Immunoglobulins, Intravenous/Immunoglobulins, Intravenous/Immunoglobulins, Intravenous/*therapeutic use ; Isoantibodies/Isoantibodies/Isoantibodies/*therapeutic use

  • Source: Haemophilia : the official journal of the World Federation of Hemophilia [Haemophilia] 2019 Jul; Vol. 25 (4), pp. e291-e293. Date of Electronic Publication: 2019 May 02.Publisher: Blackwell Science Country of Publication: England NLM ID: 9442916 Publication Model: Print-Electronic Cited Medium: Internet ISSN:

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Academic Journal

Prophylaxis with FEIBA in paediatric patients with haemophilia A and inhibitors.

Subjects: Premedication*; Blood Coagulation Factor Inhibitors/Blood Coagulation Factor Inhibitors/Blood Coagulation Factor Inhibitors/*immunology ; Blood Coagulation Factors/Blood Coagulation Factors/Blood Coagulation Factors/*therapeutic use

  • Source: Haemophilia : the official journal of the World Federation of Hemophilia [Haemophilia] 2015 May; Vol. 21 (3), pp. 358-364. Date of Electronic Publication: 2015 Jan 21.Publisher: Blackwell Science Country of Publication: England NLM ID: 9442916 Publication Model: Print-Electronic Cited Medium: Internet ISSN:

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Academic Journal

Prompt immune tolerance induction at inhibitor diagnosis regardless of titre may increase overall success in haemophilia A complicated by inhibitors: experience of two U.S. centres.

Subjects: Immune Tolerance*; Blood Coagulation Factor Inhibitors/Blood Coagulation Factor Inhibitors/Blood Coagulation Factor Inhibitors/*immunology ; Factor VIII/Factor VIII/Factor VIII/*immunology

  • Source: Haemophilia : the official journal of the World Federation of Hemophilia [Haemophilia] 2015 May; Vol. 21 (3), pp. 365-373. Date of Electronic Publication: 2015 Jan 11.Publisher: Blackwell Science Country of Publication: England NLM ID: 9442916 Publication Model: Print-Electronic Cited Medium: Internet ISSN:

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Academic Journal

Hybrid human-porcine factor VIII proteins partially escape the inhibitory effects of anti-factor VIII inhibitor alloantibodies having A2 or C2 domain specificity.

  • Authors : Mizumachi K; Department of Pediatrics, Nara Medical University, Kashihara, Nara, Japan.; Nakajima Y

Subjects: Hemophilia A*/Hemophilia A*/Hemophilia A*/drug therapy ; Hemophilia A*/Hemophilia A*/Hemophilia A*/genetics ; Factor VIII*

  • Source: Haemophilia : the official journal of the World Federation of Hemophilia [Haemophilia] 2024 Jan; Vol. 30 (1), pp. 140-150. Date of Electronic Publication: 2023 Dec 06.Publisher: Blackwell Science Country of Publication: England NLM ID: 9442916 Publication Model: Print-Electronic Cited Medium: Internet ISSN:

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Academic Journal

Impact of haemophilia with inhibitors on caregiver burden in the United States.

Subjects: Blood Coagulation Factor Inhibitors* ; Cost of Illness* ; Isoantibodies*

  • Source: Haemophilia : the official journal of the World Federation of Hemophilia [Haemophilia] 2014 Nov; Vol. 20 (6), pp. 822-30. Date of Electronic Publication: 2014 Oct 02.Publisher: Blackwell Science Country of Publication: England NLM ID: 9442916 Publication Model: Print-Electronic Cited Medium: Internet ISSN:

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Editorial & Opinion

Adult haemophilia A patients with inhibitors: successful immune tolerance induction with a single FVIII/VWF product.

  • Authors : Rangarajan S; Centre for Haemostasis & Thrombosis, Guy's & St Thomas' NHS Trust, London, UK; Hampshire Hospitals NHS Trust, Basingstoke, UK.

Subjects: Blood Coagulation Factor Inhibitors/Blood Coagulation Factor Inhibitors/Blood Coagulation Factor Inhibitors/*immunology ; Factor VIII/Factor VIII/Factor VIII/*immunology ; Hemophilia A/Hemophilia A/Hemophilia A/*immunology

  • Source: Haemophilia : the official journal of the World Federation of Hemophilia [Haemophilia] 2014 Nov; Vol. 20 (6), pp. e414-7. Date of Electronic Publication: 2014 Oct 21.Publisher: Blackwell Science Country of Publication: England NLM ID: 9442916 Publication Model: Print-Electronic Cited Medium: Internet ISSN:

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Academic Journal

Native plasma-derived FVIII/VWF complex has lower sensitivity to FVIII inhibitors than the combination of isolated FVIII and VWF proteins. Impact on Bethesda assay titration of FVIII inhibitors.

  • Authors : Bravo MI; Research and Development Area, Instituto Grifols S.A., Parets del Vallès, Barcelona, Spain.; Da Rocha-Souto B

Subjects: Blood Coagulation Factor Inhibitors/Blood Coagulation Factor Inhibitors/Blood Coagulation Factor Inhibitors/*blood ; Factor VIII/Factor VIII/Factor VIII/*pharmacokinetics ; Hemophilia A/Hemophilia A/Hemophilia A/*blood

  • Source: Haemophilia : the official journal of the World Federation of Hemophilia [Haemophilia] 2014 Nov; Vol. 20 (6), pp. 905-11. Date of Electronic Publication: 2014 Aug 25.Publisher: Blackwell Science Country of Publication: England NLM ID: 9442916 Publication Model: Print-Electronic Cited Medium: Internet ISSN:

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Report

Long-term treatment course of a patient with mild haemophilia A who developed a high titre factor VIII inhibitor.

  • Authors : Iioka F; Department of Hematology, Tenri Hospital, Tenri, Nara, Japan.; Shimomura D

Subjects: Blood Coagulation Factor Inhibitors/Blood Coagulation Factor Inhibitors/Blood Coagulation Factor Inhibitors/*immunology ; Factor VIII/Factor VIII/Factor VIII/*immunology ; Factor VIII/Factor VIII/Factor VIII/*therapeutic use

  • Source: Haemophilia : the official journal of the World Federation of Hemophilia [Haemophilia] 2014 Nov; Vol. 20 (6), pp. e402-4.Publisher: Blackwell Science Country of Publication: England NLM ID: 9442916 Publication Model: Print Cited Medium: Internet ISSN: 1365-2516

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Academic Journal

Inhibitors - cellular aspects and novel approaches for tolerance.

  • Authors : Scott DW; Department of Medicine, Uniformed Services, University for the Health Sciences, Bethesda, MD, USA.

Subjects: Factor IX/Factor IX/Factor IX/*immunology ; Factor VIII/Factor VIII/Factor VIII/*immunology ; Hemophilia A/Hemophilia A/Hemophilia A/*immunology

  • Source: Haemophilia : the official journal of the World Federation of Hemophilia [Haemophilia] 2014 May; Vol. 20 Suppl 4, pp. 80-6.Publisher: Blackwell Science Country of Publication: England NLM ID: 9442916 Publication Model: Print Cited Medium: Internet ISSN: 1365-2516

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Academic Journal

Epidemiological aspects of inhibitor development redefine the clinical importance of inhibitors.

  • Authors : van den Berg HM; Julius Center for Health Sciences and Primary Care, University Medical Center Utrecht, Utrecht, the Netherlands.

Subjects: Factor VIII/Factor VIII/Factor VIII/*immunology ; Factor VIII/Factor VIII/Factor VIII/*therapeutic use ; Hemophilia A/Hemophilia A/Hemophilia A/*drug therapy

  • Source: Haemophilia : the official journal of the World Federation of Hemophilia [Haemophilia] 2014 May; Vol. 20 Suppl 4, pp. 76-9.Publisher: Blackwell Science Country of Publication: England NLM ID: 9442916 Publication Model: Print Cited Medium: Internet ISSN: 1365-2516

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